The Science Journal of the American Association for Respiratory Care

1995 OPEN FORUM Abstracts

CARDIAC STATUS IN A GROUP OF LONG TERM VENTILATED PERSONS SUFFERING FROM DUCHENNES MUSCULAR DYSTROPHY(DMD).

Ole Norregaard & Bent Juhl. Danish Respiratory Center West, Arhus University Hospital, Arhus, Denmark.

Cardiac status (CS) has gained increasing importance as a predictor of survival in DMD-patients as the natural cause of death from respiratory failure has been overcome by long term mechanical ventilation. The aim of this paper is to report CS in a group of 20 DMD-patients, aged 24.6 +/- 5.3 years (mean +/-SD) who have been ventilated for 3.3 +/- 1.4 years. Eighteen via an uncuffed tracheostomy tube 20.9 +/- 5.8 hours per day and 2 using the BiPAP (Respironics) nine hours per day. Echocardiography was normal in 12 persons, 1 showed a thin wall of the left ventricle, 2 slightly to moderately dilated right ventricle, 1 universal hypokinesia with ejection fraction of 10-20 % (died), 1 abnormal septal motion, 1 dilated and hypokinetic left ventricle, 1 slight global hypocontractility and 1 prolapse of posterior mitral valve. ECG was normal in 9 persons, right bundle branch block was found in 6 persons, Q_{II, III, V3-6} in 4, right hypertrophy in 4 and ST-depression in 1 person. Conclusion: several years after death probably would have occurred from respiratory failure, 60% of these DMD-patients showed no signs of cardiac disease as measured by echocardiography and only 10% presented severe changes. Forty-five presented a normal ECG.

OF-95-217

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